Fontan F, Baudet E. Surgical repair of tricuspid atresia. Thorax. 1971;26:240.
PubMed PubMed Central CAS Google Scholar
Kreutzer G, Galíndez E, Bono H, et al. An operation for the correction of tricuspid atresia. J Thorac Cardiovasc Surg. 1973;66:613–21.
Gewillig M, Salaets T, de Bruaene AV, et al. How cardiac output is controlled in a fontan circulation: an update. Interdiscip Cardiovasc Thorac Surg. 2025;40:ivae183.
PubMed PubMed Central Google Scholar
Baumgartner H, Backer JD, Babu-Narayan SV, et al. 2020 ESC guidelines for the management of adult congenital heart disease. Eur Heart J. 2020;42:563–645.
van Melle JP, Wolff D, Hörer J, et al. Surgical options after fontan failure. Heart. 2016;102:1127–33.
Australia and new zealand fontan registry. 2016. https://www.fontanregistry.com/annual-reports.
Arrigoni SC, IJsselhof R, Postmus D, et al. Long-term outcomes of atrioventricular septal defect and single ventricle: a multicenter study. J Thorac Cardiovasc Surg. 2022;163:1166–75.
Soghoyan KZ, Guglin M. Durable ventricular assist device in adult patients with single ventricle: a systematic literature review. Hear Fail Rev. 2024;29:707–11.
Mascio CE. Mechanical support of the failing fontan circulation. Semin Thorac Cardiovasc Surg. 2021;33:454–8.
Téllez L, Payancé A, Tjwa E, et al. EASL-ERN position paper on liver involvement in patients with fontan-type circulation. J Hepatol. 2023;79:1270–301.
Jitta DJ, Wagenaar LJ, Mulder BJM, et al. Three cases of hepatocellular carcinoma in fontan patients: review of the literature and suggestions for hepatic screening. Int J Cardiol. 2016;206:21–6.
Daniels CJ, Bradley EA, Landzberg MJ, et al. Fontan-associated liver disease proceedings from the american college of cardiology stakeholders meeting, october 1 to 2, 2015, washington DC. J Am Coll Cardiol. 2017;70:3173–94.
Lewis MJ, Reardon LC, Aboulhosn J, et al. Clinical outcomes of adult fontan-associated liver disease and combined heart-liver transplantation. J Am Coll Cardiol. 2023;81:2149–60.
van Leeuwen OB, Brüggenwirth IMA, de Kleine RHJ, et al. Machine perfusion of donation after circulatory death liver and lungs before combined liver-lung transplantation. Transplant Direct. 2021;7:e718.
PubMed PubMed Central Google Scholar
Brüggenwirth IMA, Lantinga VA, Lascaris B, et al. Prolonged hypothermic machine perfusion enables daytime liver transplantation—an IDEAL stage 2 prospective clinical trial. EClinicalMedicine. 2024;68:102411.
PubMed PubMed Central Google Scholar
Brüggenwirth IMA, Mueller M, Lantinga VA, et al. Prolonged preservation by hypothermic machine perfusion facilitates logistics in liver transplantation: a European observational cohort study. Am J Transplant. 2022;22:1842–51.
PubMed PubMed Central Google Scholar
Emamaullee J, Zaidi AN, Schiano T, et al. Fontan-associated liver disease: screening, management, and transplant considerations. Circulation. 2020;142:591–604.
PubMed PubMed Central Google Scholar
Elder RW, McCabe NM, Hebson C, et al. Features of portal hypertension are associated with major adverse events in fontan patients: the VAST study. Int J Cardiol. 2013;168:3764–9.
PubMed PubMed Central Google Scholar
Rodriguez DS, Mao C, Mahle WT, et al. Pretransplantation and post-transplantation liver disease assessment in adolescents undergoing isolated heart transplantation for fontan failure. J Pediatr. 2021;229:78–85.e2.
Simpson KE, Esmaeeli A, Khanna G, et al. Liver cirrhosis in Fontan patients does not affect 1‑year post-heart transplant mortality or markers of liver function. J Hear Lung Transplant. 2014;33:170–7.
Hofferberth SC, Singh TP, Bastardi H, et al. Liver abnormalities and post-transplant survival in pediatric fontan patients. Pediatr Transplant. 2017;21:e13061.
Amdani S, Simpson KE, Thrush P, et al. Hepatorenal dysfunction assessment with the MELD-XI score predicts worse survival following transplant in pediatric fontan patients. J Thorac Cardiovasc Surg. 2022;163:1462–73.
Kobashigawa J, VanWagner LB, Hall S, et al. Summary of a consensus conference on heart-liver transplantation. Am J Transplant. 2024;24:380–90.
Munsterman ID, Duijnhouwer AL, Kendall TJ, et al. The clinical spectrum of fontan-associated liver disease: results from a prospective multimodality screening cohort. Eur Heart J. 2019;40:1057–68.
Emamaullee J, Khan S, Weaver C, et al. Non-invasive biomarkers of fontan-associated liver disease. JHEP Rep. 2021;3:100362.
PubMed PubMed Central Google Scholar
Vaikunth SS, Higgins JP, Concepcion W, et al. Does liver biopsy accurately measure fibrosis in fontan-associated liver disease? A comparison of liver biopsy pre-combined heart and liver transplant and liver explant post-transplant. Clin Transplant. 2020;34:e14120.
Dronavalli V, Clark S. Combined heart–liver transplantation in the UK. Ann R Coll Surg Engl. 2023;105:476.
Tracy KM, Matsuoka LK, Alexopoulos SP. Update on combined heart and liver transplantation: evolving patient selection, improving outcomes, and outstanding questions. Curr Opin Organ Transplant. 2023;28:104–9.
Wong TW, Gandhi MJ, Daly RC, et al. Liver allograft provides immunoprotection for the cardiac allograft in combined heart–liver transplantation. Am J Transplant. 2016;16:3522–31.
Plappert L, Edwards S, Senatore A, et al. The epidemiology of persons living with fontan in 2020 and projections for 2030: development of an epidemiology model providing multinational estimates. Adv Ther. 2022;39:1004–15.
Murtuza B, Hermuzi A, Crossland DS, et al. Impact of mode of failure and end-organ dysfunction on the survival of adult fontan patients undergoing cardiac transplantation. Eur J Cardiothorac Surg. 2017;51:135–41.
Bouchardy J, Meyer P, Yerly P, et al. Regression of advanced liver fibrosis after heart transplantation in a patient with prior fontan surgery for complex congenital heart disease. Circulation Hear Fail. 2018;11:e3754.
Elde S, Brubaker AL, Than PA, et al. Operative technique of donor organ procurement for en bloc heart-liver transplantation. Transplantation. 2021;105:2661–5.
Hill AL, Maeda K, Bonham CA, et al. Pediatric combined heart–liver transplantation performed en bloc: a single-center experience. Pediatr Transplant. 2012;16:392–7.
Kittleson MM, Sharma K, Brennan DC, et al. Dual-organ transplantation: indications, evaluation, and outcomes for heart-kidney and heart-liver transplantation: a scientific statement from the American heart association. Circulation. 2023;148:622–36.
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