Humbert M, Kovacs G, Hoeper MM et al (2022) 2022 ESC/ ERS guidelines for the diagnosis and treatment of pulmonary hypertension developed by the task force for the diagnosis and treatment of (ESC) and the European Respiratory Society (ERS). Eur Heart J 43(38):3618–3731

CAS  PubMed  Google Scholar 

Frank BS, Ivy DD (2020) Pediatric pulmonary arterial hypertension. Pediatr Clin North Am 67(5):903–921

PubMed  Google Scholar 

Kovacs G, Bartolome S, Denton CP et al (2024) Definition, classification and diagnosis of pulmonary hypertension. Eur Respir J 64(4):2401324

CAS  PubMed  PubMed Central  Google Scholar 

Berger RMF, Beghetti M et al (2012) Clinical features of paediatric pulmonary hypertension: a registry study. Lancet 379(9815):537–546

PubMed  PubMed Central  Google Scholar 

Moledina S, Hislop AA, Foster H et al (2010) Childhood idiopathic pulmonary arterial hypertension: a national cohort study. Heart 96(17):1401–1406

CAS  PubMed  Google Scholar 

Barst RJ, McGoon MD, Elliott CG et al (2012) Survival in childhood pulmonary arterial hypertension: insights from the registry to evaluate early and long-term pulmonary arterial hypertension disease management. Circulation 125(1):113–122

PubMed  Google Scholar 

Benza RL, Miller DP, Gomberg-Maitland M et al (2010) Predicting survival in pulmonary arterial hypertension: insights from the registry to evaluate early and long-term pulmonary arterial hypertension disease management (REVEAL). Circulation 122(2):164–172

PubMed  Google Scholar 

Lim Y, Low T, Chan SP et al (2021) Does pulmonary artery pulsatility index predict mortality in pulmonary arterial hypertension? ESC Heart Fail 8:3835–44

PubMed  PubMed Central  Google Scholar 

Kang G, Ha R, Banerjee D (2016) Pulmonary artery pulsatility index predicts right ventricular failure after left ventricular assist device implantation. J Hear Lung Transplant 35(1):67–73

Google Scholar 

Rong LQ, Rahouma M, Neuburger PJ et al (2020) Use of pulmonary artery pulsatility index in cardiac surgery. J Cardiothorac Vasc Anesth 34(5):1220–1225

PubMed  Google Scholar 

Dardi F, Boucly A, Benza R et al (2024) Risk stratification and treatment goals in pulmonary arterial hypertension. Eur Respir J. https://doi.org/10.1183/13993003.01323-2024

Article  PubMed  PubMed Central  Google Scholar 

Lokhorst C, van der Werf S, Berger RMF, Douwes JM (2022) Risk stratification in adult and pediatric pulmonary arterial hypertension: a systematic review. Front Cardiovasc Med 9:1035453

PubMed  PubMed Central  Google Scholar 

Ivy D, Rosenzweig EB, Abman SH et al (2024) Embracing the challenges of neonatal and paediatric pulmonary hypertension. Eur Respir J. https://doi.org/10.1183/13993003.01345-2024

Article  PubMed  PubMed Central  Google Scholar 

Hoeper MM, Kramer T, Pan Z et al (2017) Mortality in pulmonary arterial hypertension: prediction by the 2015 European pulmonary hypertension guidelines risk stratification model. Eur Respir J 50(2):1700740

PubMed  Google Scholar 

Qian Y, Quan R, Chen X et al (2023) Characteristics, long-term survival, and risk assessment of pediatric pulmonary arterial hypertension in China insights from a national multicenter prospective registry. Chest 163(6):1531–1542

CAS  PubMed  Google Scholar 

Mazimba S, Welch TS, Mwansa H et al (2020) Haemodynamically derived pulmonary artery pulsatility index predicts mortality in pulmonary arterial hypertension. Heart Lung Circ 28(5):752–60

Google Scholar 

Morine KJ, Kiernan MS, Pham DT et al (2016) Pulmonary artery pulsatility index is associated with right ventricular failure after left ventricular assist device surgery. J Card Fail 22(2):110–116

PubMed  Google Scholar 

Cesini S, Bhagra S, Pettit SJ (2020) Low pulmonary artery pulsatility index is associated with adverse outcomes in ambulatory patients with advanced heart failure. J Card Fail 26(4):352–359

PubMed  Google Scholar 

Korabathina R, Heffernan KS, Paruchuri V et al (2012) The pulmonary artery pulsatility index identifies severe right ventricular dysfunction in acute inferior myocardial infarction. Catheter Cardiovasc Interv 80(4):593–600

PubMed  Google Scholar 

Vonk Noordegraaf A, Chin KM, Haddad F et al (2019) Pathophysiology of the right ventricle and of the pulmonary circulation in pulmonary hypertension: an update. Eur Respir J 53(1):1801900

PubMed  PubMed Central  Google Scholar 

Smits FE, Lokhorst C, Haarman MG et al (2024) The pulmonary artery pulsatility index provides no additional prognostic information in pediatric pulmonary arterial hypertension. Children. https://doi.org/10.3390/children11101152

Article  PubMed  PubMed Central  Google Scholar 

Raymer DS, Moreno JD, Sintek MA et al (2019) The combination of tricuspid annular plane systolic excursion and HeartMate risk score predicts right ventricular failure after left ventricular assist device implantation. ASAIO J 65(3):247–251

PubMed  PubMed Central  Google Scholar 

Kazimierczyk R, Kazimierczyk E, Knapp M et al (2021) Echocardiographic assessment of right ventricular–arterial coupling in predicting prognosis of pulmonary arterial hypertension patients. J Clin Med. 10(13):2995

PubMed  PubMed Central  Google Scholar 

Colalillo A, Hoffmann-Vold AM, Pellicano C et al (2023) The role of TAPSE/sPAP ratio in predicting pulmonary hypertension and mortality in the systemic sclerosis EUSTAR cohort. Autoimmun Rev 22(4):103290

PubMed  Google Scholar